Nga Whakamatau Porphyrin

Toka Te Manawa

• He aha nga whakamātautau porphyrin?
• Hei aha ma raatau?
• He aha i hiahia ai ahau ki te whakamatautau porphyrin?
• Ka ahatia i te wa o te whakamatautau porphyrin?
• Me mahi e au tetahi mea hei whakareri mo te whakamatautau?
• He raru pea mo nga whakamatautau porphyrin?
• He aha te tikanga o nga hua?
• He mea ano e hiahia ana ahau kia mohio mo nga whakamatautau porphyrin?
• Tohutoro

He aha nga whakamātautau porphyrin?

Ko nga whakamatautau porphyrin e mehua ana i te taumata o nga porphyrins i roto i o toto, mimi, o te waatea ranei. Ko nga Porphyrins he matū hei awhina i te hemoglobin, he momo momo pūmua i roto i o toto toto whero. Ma te hemoglobin e kawe te oxygen mai i o pungarehu ki etahi atu o to tinana.

He mea noa te iti o te porphyrins i roto i o toto me etahi atu wai o te tinana. Engari ko te nui o te porphyrin tera pea he momo porphyria koe. Ko te Porphyria he raru onge ka raru pea te hauora. I te nuinga o te waa ka wehea a Porphyria ki nga waahanga e rua:

• He porphyrias kino, e pa ana ki te punaha pukaha ka puta nga tohu puku
• Porphyrias Cutaneous, hei tohu i nga tohu o te kiri ka pa ana koe ki te ra

Ko etahi porphyrias e pa ana ki te punaha io me te kiri.

Ko etahi ingoa: protoporphyrin; protoporphyrin, toto; protoporhyrin, kumete; porphyrins, paru; uroporphyrin; porphyrins, mimi; Whakamātautau Mauzerall-Granick; waikawa; ALA; porphobilinogen; PBG; protoporphyrin erythrocyte koreutu; porphyrins erythrocyte hautanga; FEP

Hei aha ma raatau?

Whakamahia ai nga whakamatautau porphyrin hei tirotiro, hei tirotiro ranei i te porphyria.

He aha i hiahia ai ahau ki te whakamatautau porphyrin?

Akene me hiahia koe ki te whakamatautau porphyrin mena ka kitea e koe he tohu o te porphyria. He rereke nga tohu mo nga momo porphyria.

Ko nga tohu o te porphyria whakapau ko:

• Te mamae o te kopu
• Tuhinga o mua
• Te whakapairuaki me te ruaki
• Mimi whero parauri ranei
• Te koretake, te mamae ranei i nga ringaringa me / ranei waewae
• Te ngoikore o te uaua
• Raruraru
• Whakakitenga

Ko nga tohu o te porphyria o te kiri kei roto:

• Te aro nui ki te ra
• Te pupuhi i te kiri kua pa atu ki te ra
• Whero me te pupuhi i runga i te kiri kitea
• Ngatata
• Nga rereketanga o te tae kiri

Akene me hiahia koe ki te whakamatautau porphyrin mena he porphyria tetahi o to whanau. Ko te nuinga o nga momo porphyria he taonga tuku iho, ko te tikanga ka paahitia te mate mai i tetahi matua ki tetahi tamaiti.

Ka ahatia i te wa o te whakamatautau porphyrin?

Ka taea te whakamatautau i nga porphyrins i roto i te toto, te mimi, te kumete ranei. Ko nga momo momo whakamatautau porphyrin e kitea ana i raro iho nei.

• Whakamatautau Toto
  • Ka tangohia e tetahi tohunga ngaio hauora tetahi tauira toto mai i te uaua i roto i to ringa, ma te whakamahi i te ngira iti. Whai muri i te kuhunga o te ngira, ka kohia he toto iti ki roto i te ipuipu, ipu ranei. Akene he iti to ngau ka puta te ngira ki waho ka puta atu ranei. Ko te tikanga ka iti ake i te rima meneti tenei.
• 24-Haora Urine Tauira
  • Ka kohia e koe to mimi katoa i roto i te waa 24-haora. Mo tenei whakamatautau, ma to kaiwhakarato ratonga hauora, to taiwhanga ranei koe e hoatu he ipu me nga tohutohu motuhake mo te kohi tauira i te kaainga. Kia mahara ki te whai i nga tohutohu katoa. Whakamahia ai tenei whakamatautau tauira mimi 24-haora na te mea ko nga rahinga o te mimi, tae atu ki te porphyrin, ka rereke puta noa i te ra. Na, ko te kohikohi i etahi tauira i te ra, ka tika ake te whakaatu i to kiko mimi.
• Whakamatau Urine Whakatau
  • Ka taea e koe te whakarato i to tauira i nga waa katoa o te ra, kaore he whakaritenga motuhake, he whakahaere ranei e hiahiatia ana. Ko tenei whakamatautau ka mahia i nga wa i te tari tari hauora, i te whare taiwhanga ranei.
• Whakamatau Tae (e kiia ana ko te protoporphyrin kei te turanga)
  • Ka kohia e koe he tauira o tau ake ka waiho ki roto i tetahi ipu motuhake. Ka tukuna atu e to kaiwhakaora hauora nga tohutohu mo te whakarite i to tauira ka tukuna atu ki tetahi taiwhanga.

Me mahi e au tetahi mea hei whakareri mo te whakamatautau?

Kaore e hiahiatia he whakaritenga motuhake mo te toto, mo te mimi ranei.

Mo te whakamatau i te tuumomo, ka tohutohungia koe kia kaua e kai kiko, kaua hoki e kai i nga rongoa whai-ahipirini mo nga ra e toru i mua o to whakamatautau.

He raru pea mo nga whakamatautau porphyrin?

He iti noa te tuponotanga ka tirohia o toto. Ka mamae pea koe, ka maru ranei koe i te waahi i maka ai te ngira, engari ko te nuinga o nga tohu ka tere wawe.

Kaore he morearea e mohiotia ana mo te mimi, mo nga waatea ranei.

He aha te tikanga o nga hua?

Mena he nui te porphyrin e kitea i roto i o toto, mimi, taahi ranei, ka tono pea to kaiwhakarato hauora kia nui ake nga whakamatautau hei whakatuturu i te tohu mate ka kitea he aha te momo porphyria kei a koe. Ahakoa kaore he rongoa mo te porphyria, ka taea te whakahaere i te mate. Ko etahi whakarereketanga o te noho me nga rongoa ka taea te aukati i nga tohu me nga raruraru o te mate. Ko te maimoatanga motuhake e pa ana ki to momo porphyria kei a koe. Mena he paatai ​​taau mo o hua, mo te porphyria ranei, korero ki to kaiwhakarato hauora.

Ako atu mo nga whakamatautau taiwhanga, awhe tohutoro, me te maarama ki nga hua.

He mea ano e hiahia ana ahau kia mohio mo nga whakamatautau porphyrin?

Ahakoa ko te nuinga o nga momo porphyria he taonga tuku iho, ka taea ano etahi atu momo porphyria te whiwhi. Ko te porphyria kua riro mai ka puta mai i nga tini ahuatanga, tae atu ki te kore whakaatu i te mata, te HIV, te mate kakati C, te nui o te kai rino, me te / te whakamahi waipiro nui ranei.

Tohutoro

1. American Porphyria Foundation [Ipurangi]. Houston: American Porphyria Foundation; c2010–2017. Mo Porphyria; [whakahua 2019 Hakihea 26]; [tata ki te 3 nga mata]. Wātea mai i: https://www.porphyriafoundation.org/for-patients/about-porphyria
2. American Porphyria Foundation [Ipurangi]. Houston: American Porphyria Foundation; c2010–2017. Nga Tohu Porphyrins me Porphyria; [whakahua 2019 Hakihea 26]; [tata ki te 6 o nga mata]. Wātea mai i: https://www.porphyriafoundation.org/for-patients/about-porphyria/testing-for-porphyria/diagnosis
3. American Porphyria Foundation [Ipurangi]. Houston: American Porphyria Foundation; c2010–2017. Nga Whakamatau Raina Tuatahi; [whakahua 2019 Hakihea 26]; [e 4 pea nga mata]. Wātea mai i: https://www.porphyriafoundation.org/for-patients/about-porphyria/testing-for-porphyria/first-line-tests
4. Hepatitis B Foundation [Ipurangi]. Doylestown (PA): Hepb.org; c2017. Nga Maama Metabolic Kua Taonga; [whakahua 2017 Tihema 20]; [tata ki te 11 nga mata]. Wātea mai i: http://www.hepb.org/research-and-programs/liver/risk-factors-for-liver-cancer/inherited-metabolic-diseases
5. Hinkle J, Cheever K. Brunner & Suddarth's Handbook of Laboratory and Diagnostic Test. 2nd Ed, Rama. Philadelphia: Wolters Kluwer Hauora, Lippincott Williams & Wilkins; c2014. Porphyrins Erythrocyte hautanga (FEP); wh. 308.
6. Nga Whakamatautau Reipa Aipurangi [Ipurangi]. American Association mo te Haumanu Haumanu; c2001–2017. Papakupu: Tauira Urine Tuturu; [whakahua 2017 Tihema 20]; [tata ki te 3 nga mata].Wātea mai i: https://labtestsonline.org/glossary#r
7. Nga Whakamatautau Reipa Aipurangi [Ipurangi]. American Association mo te Haumanu Haumanu; c2001–2017. Nga Whakamatau Porphyrin; [whakahoutia 2017 Tihema 20; whakahuahia 2017 Tihema 20]; [tata ki te 3 nga mata]. Wātea mai i: https://labtestsonline.org/tests/porphyrin-tests
8. Mayo Clinic [Ipurangi]. Mayo Foundation mo te Whakaakoranga Hauora me te Rangahau; c1998–2017. Porphyria: Nga Tohu me nga Take; 2017 Nov 18 [whakahua 2017 Tihema 20]; [tata ki te 3 nga mata]. Wātea mai i: https://www.mayoclinic.org/diseases-conditions/porphyria/symptoms-causes/syc-20356066
9. Mayo Clinic: Mayo Medical Laboratories [Ipurangi]. Mayo Foundation mo te Whakaakoranga Hauora me te Rangahau; c1995–2017. ID Whakamatautau: FQPPS: Porphyrins, Feces: Tirohanga; [whakahua 2017 Tihema 20]; [tata ki te 2 nga mata]. Wātea mai i: https://www.mayomedicallaboratories.com/test-catalog/Overview/81652
10. Mayo Clinic: Mayo Medical Laboratories [Ipurangi]. Mayo Foundation mo te Whakaakoranga Hauora me te Rangahau; c1995–2017. ID Whakamatautau: FQPPS: Porphyrins, Feces: Tauira; [whakahua 2017 Tihema 20]; [tata ki te 3 nga mata]. Wātea mai i: https://www.mayomedicallaboratories.com/test-catalog/Specimen/81652
11. Merck Manual Kaihoko Putanga [Ipurangi]. Kenilworth (NJ): Merck & Co. Inc.; c2017. Porphyria Puta noa; [whakahua 2017 Tihema 20]; [tata ki te 3 nga mata]. Wātea mai i: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorder/porphyrias/acute-intermittent-porphyria
12. Merck Manual Kaihoko Putanga [Ipurangi]. Kenilworth (NJ): Merck & Co. Inc.; c2017. Tirohanga o Porphyria; [whakahua 2017 Tihema 20]; [tata ki te 2 nga mata]. Wātea mai i: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorder/porphyrias/overview-of-porphyria
13. Merck Manual Kaihoko Putanga [Ipurangi]. Kenilworth (NJ): Merck & Co. Inc.; c2017. Porphyria Cutanea Tarda; [whakahua 2017 Tihema 20]; [tata ki te 3 nga mata]. Wātea mai i: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorder/porphyrias/porphyria-cutanea-tarda
14. National Heart, Lung, and Blood Institute [Ipurangi]. Bethesda (MD): Te Tari Hauora me nga Ratonga Tangata a U.S. Nga Whakamatau Toto; [whakahua 2017 Tihema 20]; [tata ki te 3 nga mata]. Wātea mai i: https://www.nhlbi.nih.gov/health-topics/blood-tests
15. National Institute of Diabetes and Digestive and Kidney Diseases [Ipurangi]. Bethesda (MD): Te Tari Hauora me nga Ratonga Tangata a U.S. Porphyria; 2014 Pepu [i whakahuahia i te 2017 Tihema 20]; [e 4 pea nga mata]. Wātea mai i: https://www.niddk.nih.gov/health-information/liver-disease/porphyria
16. Whare Wananga o Rochester Medical Center [Ipurangi]. Rochester (NY): Whare Wananga o Rochester Medical Center; c2017. Encyclopedia Hauora: Porphyrins (Urine); [whakahua 2017 Tihema 20]; [tata ki te 2 nga mata]. Wātea mai i: https://www.urmc.rochester.edu/encyclopedia/content.aspx?contenttypeid=167&contentid;=porphyrins_urine

Ko nga korero kei tenei papaanga kaua e whakamahia hei whakakapi mo te tiaki ngaio ngaio, tohutohu ranei. Whakapa atu ki te kaiwhakarato hauora mena he paatai ​​taau mo to hauora.