Kaitito: Virginia Floyd
Tuhinga O Mua: 12 Here-Turi-Kōkā 2021
Rā Whakahou: 22 Hune 2024
Anonim
Current Management of Patients with Acquired von Willebrand Syndrome (AVWS): a 2016 update
Ataata: Current Management of Patients with Acquired von Willebrand Syndrome (AVWS): a 2016 update

Ko te mate a Von Willebrand te tino mate toto e heke iho nei.

Ko te mate o Von Willebrand na te ngoikoretanga o te take von Willebrand. Ko te take o Von Willebrand te awhina i nga peara toto kia piri ngatahi ka piri ki te pakitara o te toto, he mea tika mo te whakaheke toto noa. He maha nga momo mate von Willebrand.

Ko te hitori o te whanau he mate toto te mea morearea tuatahi.

Ko nga tohu ka uru atu ki:

  • Te whakaheke toto totika noa
  • Tuhinga o mua
  • Pakaru
  • Nosebleeds
  • Pakihi kiri

Panui: Ko te nuinga o nga waahine he taumaha nui, he roa ranei te whakaheke toto kaore he mate von Willebrand.

Ko te mate a Von Willebrand he uaua ki te tohu. Ko nga taumata take iti o von Willebrand me te whakaheke toto kaore i te kii he mate von Willebrand koe.

Ko nga whakamatautau ka taea te whakatau kia kitea tenei mate ko te:

  • Te wa toto
  • Patoto toto
  • Tauwehenga VIII taumata
  • Tātari mahi papahono
  • Tatauranga peera
  • Whakamatau i te cofactor ristocetin
  • Nga whakamatautau motuhake a Von Willebrand

Ko te maimoatanga ka uru ki te DDAVP (desamino-8-arginine vasopressin). He rongoa hei whakapiki i te taumata von von Willebrand me te whakaiti i te tuponotanga o te whakaheke toto.


Heoi, kaore te DDAVP e mahi mo nga momo mate von Willebrand. Me mahi nga whakamatautau hei whakatau he aha te momo von Willebrand kei a koe. Mena ka whai pokanga koe, ma te taakuta pea e tuku DDAVP ki a koe i mua o te pokanga kia kite koe mena kua piki ake to taumata von Willebrand.

Ko te raau taero Alphanate (antihemophilic factor) ka whakaaetia hei whakaiti i te whakaheke toto i nga taangata e pangia ana e te mate me poka tetahi atu tikanga haukoti ranei.

Ka taea hoki te whakamahi i te waipiro toto etahi waahanga VIII ranei hei whakarite ki te whakaheke toto.

Ka heke te toto i te wa e hapu ana. Ko nga waahine he penei te ahua kaore i te nui te toto i te wa e whanau ana.

Ko tenei mate ka tukuna e nga whanau. Ma te tuku whakaaro tuku iho e awhina te hunga maatua kia mohio ki te raru o a raatau tamariki.

Ka mate te toto i muri o te pokanga, ka toia ranei to niho.

Ko te Aspirin me etahi atu rongoa anti-mumura nonsteroidal (NSAIDs) ka kino rawa atu tenei mate. Kaua e kainga enei rongoa me te kore korero ki te kaitautoko hauora.


Karangahia to kaiwhakarato mena ka rere te toto kaore he take.

Mena he mate koe von Willebrand a kua whakaritea koe mo te pokanga, kei te tupono ranei koe i tetahi aituā, kia mahara koe ko to whanau ranei kia korero ki nga kaiwhakarato mo to mate.

Te mate toto - von Willebrand

  • Te whakaheke toto
  • Pakihi toto

Waipuke VH, Scott JP. Mate Von Willebrand. I roto i: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Pukapuka Pukapuka a Whakatata mo nga Pediatrics. 21st ed. Philadelphia, PA: Elsevier; 2020: chap 504.

James P, Rydz N. Hanganga, koiora, me nga iranga o von Willebrand factor. I roto i: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Maatauranga Maatauranga me te Mahi. Ed 7. Philadelphia, PA: Elsevier; 2018: chap 138.


Neff AT. Ko te mate Von Willebrand me nga ngoikoretanga hemorrhagic o te peera me te mahi ngongo. I roto i: Goldman L, Schafer AI, eds. Te rongoa Goldman-Cecil. 26th ed. Philadelphia, PA: Elsevier; 2020: chap 164.

Samuels P. Hematologic raruraru o te haputanga. I roto i: Landon MB, Galan HL, Jauniaux ERM et al, eds. Gabbe's Obstetrics: Nga Maamaa me nga Whakanuia Raru. 8th ed. Philadelphia, PA: Elsevier; 2021: chap 49.

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